α1‐Antitrypsin deficiency‐associated panniculitis: case report and review of treatment options
Identifieur interne : 001E21 ( Main/Exploration ); précédent : 001E20; suivant : 001E22α1‐Antitrypsin deficiency‐associated panniculitis: case report and review of treatment options
Auteurs : Pg Ortiz [Danemark] ; Bg Skov [Danemark] ; E. BenfeldtSource :
- Journal of the European Academy of Dermatology and Venereology [ 0926-9959 ] ; 2005-07.
English descriptors
- Teeft :
- Acad dermatol, Acta derm venereol, Alpha panniculitis, Arch dermatol, Case report, Changes histiocytic cells, Collagen bundles, Dapsone, Dermatol, Elastin, English literature, European academy, Frequent mutation, Giant cells, Insufficient inhibition, Intravenous prolastin, Lesion, Liver disease, Liver function tests, Liver transplantation, Neutrophil, Nodule, Oral dapsone therapy, Panlobular emphysema, Panniculitis, Persistent cutaneous vasculitis, Possible mechanisms, Primary lesion, Protease, Serine proteases, Serum levels, Severe panniculitis, Skin symptoms, Total absence, Venereology jeadv.
Abstract
α1‐Antitrypsin deficiency, a relatively frequent mutation in the population, is associated with the development of panlobular emphysema and liver cirrhosis. The deficiency is in rare cases associated with the development of panniculitis, and very differentiated clinical courses have been reported in the literature. We report a case of panniculitis in a patient with α1‐antitrypsin deficiency and describe briefly the pathophysiology of the disease and current treatment possibilities.
Url:
DOI: 10.1111/j.1468-3083.2005.01194.x
Affiliations:
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Le document en format XML
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